What is Fibrous Dysplasia?

Fibrous Dysplasia refers to a benign bony tumor located in some portion of the craniofacial skeleton, caused by an overgrowth of certain kinds of cell parts that do not behave normally—but grow in number for no reason. 

Typically we see the initial growth in early childhood through the teenage years, with progressive but slow growth. Sometimes, for example, a parent will notice a bump on the forehead which gradually increases in size. Or, we might observe that the eye on one side is asymmetrical compared to the normal position, due to the tumor growing in that area and pushing the eye out of place; the child may have double vision when the tumor is crowding the eye(s). In fact, wherever it grows in the facial region, it will eventually displace the surrounding structures and show up as a mass or lump in that area.

At the most appropriate time, we completely remove the tumor along with whatever portion of skeletal bone involved, and restructure or complete a bone graft to build the area up to a normal shape and appearance. We can also release the optic nerve if compressed. This is typically a highly successful treatment with minimal disability or malformation afterwards. 

What is Neurofibromatics?

Neurofibromatosis grows around the nerve cells/sheaths and affects all nearby tissues: skin, the layer below the skin (subcutaneous) and bone. It may become evident in any of three forms: flat lesions that follow a nerve and cause enlargement of surrounding tissues; small, round nodules present in groups; or massive overgrowths of skin and associated soft tissues.

 

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